Prevention of sudden cardiac death in childhood-onset hypertrophic cardiomyopathy

Sudden cardiac death (SCD) is the most common cause of in children with HCM. Although recent population-based studies have shown that SCD rates are lower than previously thought, it still occurs more frequently adult patients, highlighting importance accurate identification those at risk. This review highlights risk factors for childhood HCM, current stratification guidelines, and novel personalized models prediction. The traditional approach to prediction childhood-onset using cumulative factor thresholds adopted by international has involved extrapolation data, but evidence demonstrated this does not accurately discriminate high-risk from low-risk individuals. In response knowledge gap, pediatric-specific been developed allow calculation individualized estimates enable a shared decision-making ICD implantation.